Show simple item record

dc.contributor.authorArkadopoulos, Nikolaosen
dc.contributor.authorKarapanos, Konstantinosen
dc.contributor.authorStafyla, V. K.en
dc.contributor.authorYiallourou, Anneza I.en
dc.contributor.authorKoureas, Andreasen
dc.contributor.authorKondi-Pafiti, Agathien
dc.contributor.authorSmyrniotis, V.en
dc.creatorArkadopoulos, Nikolaosen
dc.creatorKarapanos, Konstantinosen
dc.creatorStafyla, V. K.en
dc.creatorYiallourou, Anneza I.en
dc.creatorKoureas, Andreasen
dc.creatorKondi-Pafiti, Agathien
dc.creatorSmyrniotis, V.en
dc.description.abstractContext Von Hippel-Lindau disease is an inherited syndrome of multiorgan neoplasia caused by a germline mutation in the von Hippel-Lindau gene and can include central nervous system tumors, renal cell carcinomas and benign pancreatic cystic tumors. Case report We report the case of a 56-year-old patient who had a past history of cerebellar hemangioblastoma and presented with abdominal pain. Imaging revealed renal tumors and multiple pancreatic tumors which caused duodenal and pancreatic duct compression. The patient was treated with a combination of radical right nephrectomy, total pancreaticoduodenectomy and splenectomy. Pathology identified a multifocal unilateral clear cell renal carcinoma which interestingly coexisted with multiple large pancreatic serous microcystic adenomas with infiltration of the fibrous capsule. Conclusion In past cases of von Hippel-Lindau disease, pancreatic adenomas with malignant transformation have not been reported. In our case, the infiltration of the fibrous capsule by parenchymal cells may indicate malignant transformation.en
dc.sourceJournal of the Pancreasen
dc.subjectAdenoma nephrectomyen
dc.subjectClear cellen
dc.subjectVon hippel-lindau diseaseen
dc.titleCombination of right nephrectomy and total pancreaticoduodenectomy for von hippel-lindau diseaseen
dc.description.endingpage272Ιατρική Σχολή / Medical SchoolΙατρική Σχολή / Medical School
dc.contributor.orcidYiallourou, Anneza I. [0000-0003-1237-1661]

Files in this item


There are no files associated with this item.

This item appears in the following Collection(s)

Show simple item record