dc.contributor.author | Arkadopoulos, Nikolaos | en |
dc.contributor.author | Karapanos, Konstantinos | en |
dc.contributor.author | Stafyla, V. K. | en |
dc.contributor.author | Yiallourou, Anneza I. | en |
dc.contributor.author | Koureas, Andreas | en |
dc.contributor.author | Kondi-Pafiti, Agathi | en |
dc.contributor.author | Smyrniotis, V. | en |
dc.creator | Arkadopoulos, Nikolaos | en |
dc.creator | Karapanos, Konstantinos | en |
dc.creator | Stafyla, V. K. | en |
dc.creator | Yiallourou, Anneza I. | en |
dc.creator | Koureas, Andreas | en |
dc.creator | Kondi-Pafiti, Agathi | en |
dc.creator | Smyrniotis, V. | en |
dc.date.accessioned | 2018-06-22T09:52:27Z | |
dc.date.available | 2018-06-22T09:52:27Z | |
dc.date.issued | 2010 | |
dc.identifier.uri | https://gnosis.library.ucy.ac.cy/handle/7/41365 | |
dc.description.abstract | Context Von Hippel-Lindau disease is an inherited syndrome of multiorgan neoplasia caused by a germline mutation in the von Hippel-Lindau gene and can include central nervous system tumors, renal cell carcinomas and benign pancreatic cystic tumors. Case report We report the case of a 56-year-old patient who had a past history of cerebellar hemangioblastoma and presented with abdominal pain. Imaging revealed renal tumors and multiple pancreatic tumors which caused duodenal and pancreatic duct compression. The patient was treated with a combination of radical right nephrectomy, total pancreaticoduodenectomy and splenectomy. Pathology identified a multifocal unilateral clear cell renal carcinoma which interestingly coexisted with multiple large pancreatic serous microcystic adenomas with infiltration of the fibrous capsule. Conclusion In past cases of von Hippel-Lindau disease, pancreatic adenomas with malignant transformation have not been reported. In our case, the infiltration of the fibrous capsule by parenchymal cells may indicate malignant transformation. | en |
dc.language.iso | eng | en |
dc.source | Journal of the Pancreas | en |
dc.subject | Adenocarcinoma | en |
dc.subject | Adenoma nephrectomy | en |
dc.subject | Clear cell | en |
dc.subject | Pancreatectomy | en |
dc.subject | Von hippel-lindau disease | en |
dc.title | Combination of right nephrectomy and total pancreaticoduodenectomy for von hippel-lindau disease | en |
dc.type | info:eu-repo/semantics/article | |
dc.description.volume | 11 | |
dc.description.issue | 3 | |
dc.description.startingpage | 270 | |
dc.description.endingpage | 272 | |
dc.author.faculty | Ιατρική Σχολή / Medical School | |
dc.author.department | Ιατρική Σχολή / Medical School | |
dc.type.uhtype | Article | en |
dc.contributor.orcid | Yiallourou, Anneza I. [0000-0003-1237-1661] | |
dc.gnosis.orcid | 0000-0003-1237-1661 | |